A Guide for Patients and Health Care Providers

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Why do I need to know about CPVT?

CPVT is an uncommon, potentially lethal, treatable cardiac channelopathy (inherited heart rhythm syndrome). It is far less common than LQTS but does affect otherwise healthy infants, children, adolescents, and adults at an unacceptably high rate. However, with increased awareness, genetic testing, and effective treatment options, CPVT can be diagnosed early and sudden death prevented. Still, this condition is often undetected prior to death and not recognized as the cause of death. Family members of individuals with unexplained death should be tested for CPVT and other genetic arrhythmias. CPVT is a treatable disorder and, with correct diagnosis and treatments, most deaths are preventable.

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